Children who have surgery for hirschsprung disease most often feel better after surgery. The surgical treatment of hirschsprung s disease in the adult or adolescent adult hirschsprung s disease remains controversial. A doctor will know if your child has hirschsprung disease based on a physical exam, a medical and family history, symptoms, and test results. A child with hirschsprung disease without complications should be followed regularly to at least age 5 years, and the pa should observe for signs of longterm postoperative complications. In this procedure, the lining of the diseased part of the colon is stripped away. Currently, apart from preventiontreatment of dehydration. Hirschsprungs disease symptoms and causes mayo clinic. Memarzadeh m, talebi a, edalaty m, hosseinpour m, vahidi n. Eighty nine patients, clinically and radiologically diagnosed with hirschsprungs disease underwent surgery and were included in the study. These nerve cells allow the intestine to relax so stool poop can pass through the intestine and out of the body. Alternativecomplementary therapies for motor symptoms. Hirschsprung s disease should be confirmed using rectal suction biopsy. Hirschsprungs disease diagnosis and treatment mayo clinic. The utility of the hematoxylin and eosin staining in.
Doctors will usually do one of two types of surgery. Also, it is known as aganglionosis because one of the main characteristics in all these patients is that they do not have ganglion cells in the rectum. Parkinsons disease handbook american parkinson disease. Neonatal congenital microvillus atrophy postgraduate medical. Hirschsprung disease is a lifethreatening illness, and treatment requires surgery.
Nhirschsprung disease remains a challenging diagnosis for many pathologists. The condition is present at birth congenital as a result of missing nerve cells in the muscles of the babys colon. But if found quickly, it can almost always be cured by surgery. Deepak singh and others published role of barium enema in the diagnosis of. Hirschsprung s disease aganglionosis hirschsprung s disease is name for harald hirschsprung, a danish pediatrician who was the first to describe this condition in 1886. Hirschsprung disease is a common cause of lower intestinal obstruction in neonates and infants. Those affected with this birth defect are missing intestinal nerve cells called ganglion cells. Stg retains its purpose of identifying medicines that are considered essential for the treatment of common disease conditions in tanzania. C 17 serial rectal irrigation should be performed before surgery to help prevent enterocolitis. For most people, hirschsprung s disease is treated with surgery to bypass the part of the colon thats lacking nerve cells. Hirschsprungs disease in neonates with special reference to. Hirschsprung s hirshsproongz disease is a condition that affects the large intestine colon and causes problems with passing stool. Hirschsprung s disease, usually diagnosed in newborns, is a birth defect that affects about l out of 5,000 individuals. Each of the procedures developed for the childhood disorder have been applied to adolescent children and adults with varying success.26 1397 911 563 203 761 1413 243 572 917 524 88 878 1323 1242 1044 903 886 31 256 1302 1581 1293 1022 1416 1440 725 1359 1487 905 408 1173 1186 516 1421 145 859 1030 8 1131 953 750 932 236 1195 1279